STAT3-dependent Regulation of CFTR and Ciliogenesis Is Essential for Mucociliary Clearance and Innate Airway Defense in Hyper-IgE Syndrome

Authors: Ling Sun, Samantha A. Walls, Hong Dang, Nancy L. Quinney, Patrick R Sears, Taraneh Sadritabrizi, Koichi Hasegawa, Kenichi Okuda, Takanori Asakura, Xiuya Chang, Meiqi Zheng, Yu Mikami, Felicia U. Dizmond, Daniela Danilova, Lynn Zhou, Anshulika Deshmukh, Deborah M Cholon, Giorgia Radicioni, Troy D. Rogers, William J. Kissner, Matthew R Markovetz, Tara N. Guhr Lee, Mark I. Gutay, Charles R Esther, Michael Chua, Barbara R Grubb, Camille Ehre, Mehmet Kesimer, David B. Hill, Lawrence E Ostrowski, Brian Button, Martina Gentzsch, Chevalia Robinson, Kenneth N. Olivier, Alexandra F Freeman, Scott H Randell, Eszter Vladar, Wanda K. O'Neal, Richard C. Boucher, Gang Chen

Published: 2025-06-13

DOI: 10.1164/rccm.202407-1415oc

Source: Full article


Abstract

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